Coronary artery anomaly

Coronary artery anomaly
Anomalous origin of the right coronary artery from the left coronary sinus by CMR with an inter-arterial, potentially dangerous course
Classification and external resources
Specialty	medical genetics
ICD-10	Q24.5
ICD-9-CM	746.85
DiseasesDB	34206
eMedicine	med/445 ped/2506
MeSH	D003330

Coronary artery anomalies (or malformation of coronary vessels) are congenital abnormalities in the coronary anatomy of the heart. By definition, these abnormalities are variants of anatomy occurring in less than 1% of the general population. They are often found in combination with other congenital heart defects. Many coronary anomalies don't cause symptoms and are recognized only at the time of autopsy.

They can be associated with sudden death.^[1] The real risk of death or the best way to treat these patients is not yet known. The Congenital Heart Surgeons' Society has started a long-term ongoing study called anomalous aortic origin of a coronary artery (AAOCA) to identify the best way to treat this defect.

References

↑ Basso C, Maron BJ, Corrado D, Thiene G (May 2000). "Clinical profile of congenital coronary artery anomalies with origin from the wrong aortic sinus leading to sudden death in young competitive athletes". J. Am. Coll. Cardiol. 35 (6): 1493–501. doi:10.1016/S0735-1097(00)00566-0. PMID 10807452.

Congenital heart defects (Q20–Q24, 745–746)

Cardiac shunt/
heart septal defect

Aortopulmonary septal defect	R→L: Double outlet right ventricle Taussig–Bing syndrome Transposition of the great vessels dextro levo Persistent truncus arteriosus Aortopulmonary window

Atrial septal defect	L→R: Sinus venosus atrial septal defect Lutembacher's syndrome

Ventricular septal defect	L→R and R→L: Eisenmenger's syndrome R→L, with other conditions: Tetralogy of Fallot

Atrioventricular septal defect	L→R: Ostium primum

Valvular heart disease/
heart chambers

Right	pulmonary valves stenosis insufficiency tricuspid valves stenosis atresia Ebstein's anomaly Hypoplastic right heart syndrome Uhl anomaly

Left	aortic valves stenosis insufficiency bicuspid mitral valves stenosis regurgitation Hypoplastic left heart syndrome

Other

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